gene 1,162 words KG: FRDA
Contents

FXN Gene (Frataxin)

🧬 Gene Info
Gene SymbolFRDA
Functionencodes a small mitochondrial protein that plays a critical role in iron-sulfur cluster (Fe-S) biogenesis, mitochondrial energy production, and cellular iron homeostasis.
Molecular Weight~14 kDa (precursor), ~8 kDa (mature)
Amino Acids210 aa
Ensembl IDENSG00000165060
GeneCardsFRDA
Human Protein AtlasFRDA
Precursor~210 amino acids
Mature form~130 amino acids after processing
Molecular weight~14 kDa (precursor), ~8 kDa (mature)
N-terminal helixMitochondrial targeting sequence (cleaved)
α-helical domainForms the core structure
β-sheet domainContains the iron-binding surface
Iron-binding sitesAcidic residues on the protein surface
Ferroxidase activityCan oxidize Fe²⁺ to Fe³⁺
Associated DiseasesALS, Ataxia, neurodegeneration
KG Connections8 knowledge graph edges
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

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