CHMP2B

Charged multivesicular body protein 2B

Score: 0.512 Price: $0.51 Low Druggability Status: active Wiki: CHMP2B
🧠 Neurodegeneration
HYPOTHESES
1
PAPERS
28
KG EDGES
172
DEBATES
1

3D Protein Structure

🧬 CHMP2B — PDB 6HRB Click to expand

Experimental structure from RCSB PDB | Powered by Mol*

Druggability & Clinical Context

Druggability
Low
Score: 0.32
Clinical Stage
Phase II
Target Class
Other
Safety
0.30
Druggability Analysis
Drug Development0.45
Structural Tractability0.70
Target Class0.50
Safety Profile0.30
Key Metrics
PDB Structures:
1
Known Drugs:
4
Approved:
0
In Clinical Trials:
3
Drug Pipeline (4 compounds)
1 Preclinical
Druggability Rationale: CHMP2B has low druggability (0.30) as a structural ESCRT-III component lacking a well-defined ligand-binding pocket, making direct small-molecule inhibition unfeasible. Current therapeutic strategies circumvent this limitation by targeting upstream regulators (autophagy enhancers, GLP-1 agonists) or modulating CHMP2B expression indirectly via antisense oligonucleotides rather than occupying a conserved binding site.
Mechanism: Therapeutic agents targeting CHMP2B would modulate ESCRT-III complex function to enhance endosomal sorting and autophagy, potentially clearing protein aggregates associated with frontotemporal dementia or compensating for loss-of-function mutations. Strategies include antisense oligonucleotides to modulate protein expression, autophagy enhancers to promote cellular clearance pathways, or small molecules that stabilize ESCRT-III complex assembly and function.
Drug Pipeline (4 compounds)
1 Preclinical
Known Drugs:
ISIS 420915 (Antisense against Tau) (phase2) — Frontotemporal Dementia associated with Progranulin mutations
BIIB078 (phase1) — C9ORF72-related frontotemporal dementia and ALS
GLP-1 Receptor Agonists (Liraglutide derivatives) (phase2) — Neuroinflammation in Frontotemporal Dementia
Autophagy modulators (Experimental compounds) (preclinical) — ESCRT-III pathway dysfunction and neurodegeneration
Structural Data:
PDB (1) ✓AlphaFold ✓Cryo-EM —
2JQK
UniProt: Q9UQN3

🧬 3D Protein Structure

🧬 CHMP2B — PDB 6HRB Click to expand interactive 3D viewer

Experimental structure from RCSB PDB | Powered by Mol* | Rotate: click+drag | Zoom: scroll

Selectivity & Safety Considerations

CHMP2B selectivity challenges stem from high homology with other ESCRT-III family members (CHMP2A, CHMP3, CHMP4); antisense and autophagy modulator approaches offer better selectivity through sequence-specific targeting. Off-target effects on general autophagy or endosomal sorting pathways represent the primary risk for systemic modulators.

3D Protein Structure

PDB: Open in RCSB AlphaFold model

Interactive 3D viewer powered by RCSB PDB / Mol*. Use mouse to rotate, scroll to zoom.

Clinical Trials (2)

Relevant trials from ClinicalTrials.gov

Active
0
Completed
1
Total Enrollment
181
By Phase
PHASE1: 2
A Study to Assess the Safety, Tolerability, and Pharmacokinetics of BIIB078 in Adults With C9ORF72-Associated Amyotrophi Completed
PHASE1 NCT03626012 n=106
Amyotrophic Lateral Sclerosis
Interventions: BIIB078, Placebo
Sponsor: Biogen | Started: 2018-09-10
Study to Assess the Safety, Tolerability, Pharmacokinetics, and Effect on Disease Progression of BIIB078 Administered to Terminated
PHASE1 NCT04288856 n=75
Amyotrophic Lateral Sclerosis
Interventions: BIIB078
Sponsor: Biogen | Started: 2020-04-28

Linked Hypotheses (1)

Lysosomal Membrane Repair Enhancement0.538

Linked Experiments (0)

No linked experiments

Scoring Dimensions

Portfolio 0.54 (25%) Druggability 0.32 (20%) Evidence 0.57 (20%) Safety 0.30 (15%) Competitive 0.65 (10%) Connectivity 0.90 (10%) 0.512 composite

Knowledge Graph (20)

activates (12)

CHMP6CHMP2BCHMP2BCHMP2ASPHK1CHMP2BTARDBPCHMP2BPINK1CHMP2B
▸ Show 7 more
LC3CHMP2BMTORCHMP2BPTENCHMP2BVCPCHMP2BTBK1CHMP2BCHMP2BOVERVIEWCHMP2BVALOSIN

associated with (2)

CHMP2BneurodegenerationOPTNCHMP2B

co discussed (6)

STX17CHMP2BCHMP2BLAMP1CHMP2BMCOLN1CHMP2BFOXO1CHMP2BIGF2R
▸ Show 1 more
CHMP2BRAB7A

Debate History (1)

Should CHMP2B (Charged multivesicular body protein 2B) be prioritized as a thera2026-04-22