| Prevalence | Estimated at 1-2 per 100,000 individuals. |
| Incidence | Approximately 2.4-4.6 cases per million person-years [@epidemiology2022]. |
| Age distribution | Can occur at any age, but peak incidence is in the 40-60 year age group. |
| Gender | Slight male predominance (approximately 1.5:1 male-to-female ratio). |
| Geographic variation | Cases have been reported worldwide with no clear ethnic predilection. |
| Granulomatous angiitis | The most common form, characterized by granulomatous inflammation with multinucleated giant cells |
| Lymphocytic vasculitis | T-lymphocyte predominant inflammation |
| Databases | OMIMOrphanetClinicalTrialsPubMed |
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