protein 3,035 words KG: TARDNABINDINGPROTEIN43
Contents

TAR DNA-Binding Protein 43 (TDP-43)

🔬 Protein Info
Gene SymbolTARDNABINDINGPROTEIN43
AliasesTARDNABINDINGPROTEIN43
Chromosome1p36.22
FunctionMediates both transcriptional repression and RNA splicing regulation
Nuclear Localization Signal (NLS)Residues 82-98, a basic region mediating importin-α/β binding
Dimerization domainEnables TDP-43 to form homodimers and higher-order oligomers
Nuclear export signal (NES)Recently identified in this region
Recognition motifRRM1 has high affinity for UG-rich sequences (TAR DNA, UG repeats)
StructureClassical RRM fold with RNP1 and RNP2 consensus sequences
Binding specificitySingle-stranded DNA and RNA, with preference for pyrimidine-rich sequences
Auxiliary RNA bindingEnhances specificity and affinity for target RNAs
Splicing regulationCritical for exon skipping events (e.g., CFTR exon 9, SMN2 exon 7)
Structural roleStabilizes RRM1 binding through inter-domain interactions
HnRNP interactionsBinds to other hnRNP proteins (A1, A2/B1, C)
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

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Related Hypotheses (21)

Liquid-Liquid Phase Separation Modifier Therapy
Score: 0.55
PARP1 Inhibition Therapy
Score: 0.74
Cross-Seeding Prevention Strategy
Score: 0.69
RNA Granule Nucleation Site Modulation
Score: 0.66
Arginine Methylation Enhancement Therapy
Score: 0.65

Related Analyses (10)

Epigenetic reprogramming in aging neurons
neurodegeneration · completed
What determines the specificity of DDR protein recruitment t
neurodegeneration · completed
How do dilncRNAs specifically drive molecular crowding and p
neurodegeneration · completed
Mitochondrial transfer between astrocytes and neurons
neurodegeneration · archived
RNA binding protein dysregulation across ALS FTD and AD
neurodegeneration · archived

Related Experiments (3)

Proposed experiment from debate on TDP-43 undergoes liquid-l
falsification · proposed · Score: 0.40
Mechanism: Progranulin Loss and TDP-43 Pathology in FTD
validation · proposed · Score: 0.40
TDP-43 PET Ligand Development for FTD and ALS
clinical · proposed · Score: 0.40

See Also (1)

Neurodegeneration
disease · KG edge: implicated_in

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